GHELLI, ANNA MARIA

GHELLI, ANNA MARIA  

FABIT - DIPARTIMENTO DI FARMACIA E BIOTECNOLOGIE  

Docenti di ruolo di IIa fascia  

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Risultati 1 - 20 di 84 (tempo di esecuzione: 0.029 secondi).
Titolo Autore(i) Anno Periodico Editore Tipo File
Adult Leigh Syndrome Associated with the m.15635T>C Mitochondrial DNA Variant Affecting the Cytochrome b (MT-CYB) Gene Tropeano, C. V.; La Morgia, C.; Achilli, A.; Iommarini, L.; Tioli, G.; Caporali, L.; Olivieri, A....; Valentino, M. L.; Liguori, R.; Barboni, P.; Martinuzzi, A.; Tonon, C.; Lodi, R.; Torroni, A.; Carelli, V.; Ghelli, A. M. 2025-01-01 INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES - 1.01 Articolo in rivista ijms-26-01116-v2.pdfijms-26-01116-s001.zip
Formation of I2+III2 supercomplex rescues respiratory chain defects Liang, C.; Padavannil, A.; Zhang, S.; Beh, S.; Robinson, D. R. L.; Meisterknecht, J.; Cabrera-Ore...fice, A.; Koves, T. R.; Watanabe, C.; Watanabe, M.; Illescas, M.; Lim, R.; Johnson, J. M.; Ren, S.; Wu, Y. J.; Kappei, D.; Ghelli, A. M.; Funai, K.; Osaka, H.; Muoio, D.; Ugalde, C.; Wittig, I.; Stroud, D. A.; Letts, J. A.; Ho, L. 2025-01-01 CELL METABOLISM - 1.01 Articolo in rivista -
Impaired plasma membrane calcium ATPase activity and mitochondrial dysfunction contribute to calcium dysregulation in Fabry disease-related painful neuropathy Formaggio, Francesco; Pizzi, Asia; Delprete, Cecilia; Pasqualini, Davide; Mataloni, Isabella; Rim...ondini, Roberto; Campolongo, Ludovica; Donadio, Vincenzo; Ghelli, Anna Maria; Liguori, Rocco; Caprini, Marco 2025-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista -
Mitochondrial chaperonin DNAJC15 promotes vulnerability to ferroptosis of chemoresistant ovarian cancer cells Miglietta, Stefano; Sollazzo, Manuela; Gherardi, Iacopo; Milioni, Sara; Cavina, Beatrice; Marchio..., Lorena; De Luise, Monica; Coada, Camelia Alexandra; Fiorillo, Marco; Perrone, Anna Myriam; Kurelac, Ivana; Gasparre, Giuseppe; Iommarini, Luisa; Ghelli, Anna Maria; Porcelli, Anna Maria 2025-01-01 OPEN BIOLOGY - 1.01 Articolo in rivista Open Biol - SM.pdf
A computational study to assess the pathogenicity of single or combinations of missense variants on respiratory complex I Rigobello L.; Lugli F.; Caporali L.; Bartocci A.; Fadanni J.; Zerbetto F.; Iommarini L.; Carelli ...V.; Ghelli A.M.; Musiani F. 2024-01-01 INTERNATIONAL JOURNAL OF BIOLOGICAL MACROMOLECULES - 1.01 Articolo in rivista 92_2024_Rigobello_IntJBiolMacromol_compressed (1).pdf1-s2.0-S0141813024038911-mmc1.pdf
Biochemical and computational approaches to dissect the effect of MT-CYB pathogenic mutations on respiratory chain activity and assembly Tioli, G; Musiani, F; Iommarini, L; Porcelli, Am; Carelli, V; Ghelli, Am 2024-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.06 Abstract in rivista -
Genetic variants affecting NQO1 protein levels impact the efficacy of idebenone treatment in Leber hereditary optic neuropathy Aleo S.J.; Del Dotto V.; Romagnoli M.; Fiorini C.; Capirossi G.; Peron C.; Maresca A.; Caporali L....; Capristo M.; Tropeano C.V.; Zanna C.; Ross-Cisneros F.N.; Sadun A.A.; Pignataro M.G.; Giordano C.; Fasano C.; Cavaliere A.; Porcelli A.M.; Tioli G.; Musiani F.; Catania A.; Lamperti C.; Marzoli S.B.; De Negri A.; Cascavilla M.L.; Battista M.; Barboni P.; Carbonelli M.; Amore G.; La Morgia C.; Smirnov D.; Vasilescu C.; Farzeen A.; Blickhaeuser B.; Prokisch H.; Priglinger C.; Livonius B.; Catarino C.B.; Klopstock T.; Tiranti V.; Carelli V.; Ghelli A.M. 2024-01-01 CELL REPORTS MEDICINE - 1.01 Articolo in rivista 2024 - Aleo - Idebenone and NQO1 - Cell reports Medicine.pdf
Mitochondrial Chaperonin MCJ Promotes Vulnerability to Ferroptosis of Chemoresistant Ovarian Cancer Cells – Dataset Stefano Miglietta; Manuela Sollazzo; Iacopo Gherardi; Sara Milioni; Beatrice Cavina; Lorena March...io; Monica De Luise; Camelia Alexandra Coada; Marco Fiorillo; Anna Myriam Perrone; Ivana Kurelac; Giuseppe Gasparre; Luisa Iommarini; Anna Maria Ghelli; Anna Maria Porcelli 2024-01-01 - - 7.05 Banche dati -
Respiratory complex I deficiency triggers OMA1-mediated integrated stress response and affects lipid homeostasis during glucose restriction Milioni, S; Sollazzo, M; Zanna, C; Kurelac, I; Tartagni, O; Gherardi, I; Ghelli, Am; Filho, Adc; ...Schulze, A; Gasparre, G; Porcelli, Am; Iommarini, L 2024-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.06 Abstract in rivista -
Use of bacterial photosynthetic vesicles to evaluate the effect of ionic liquids on the permeability of biological membranes Bin, Tancredi; Venturoli, Giovanni; Ghelli, Anna Maria; Francia, Francesco 2024-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOMEMBRANES - 1.01 Articolo in rivista BBAbiomembranesIonicLiquids2024.pdf
Inducing respiratory complex I impairment elicits an increase in PGC1α in ovarian cancer De Luise, Monica; Sollazzo, Manuela; Lama, Eleonora; Coadă, Camelia Alexandra; Bressi, Licia; Ior...io, Maria; Cavina, Beatrice; D’Angelo, Luigi; Milioni, Sara; Marchio, Lorena; Miglietta, Stefano; Coluccelli, Sara; Tedesco, Greta; Ghelli, Anna; Lemma, Silvia; Perrone, Anna Myriam; Kurelac, Ivana; Iommarini, Luisa; Porcelli, Anna Maria; Gasparre, Giuseppe 2022-01-01 SCIENTIFIC REPORTS - 1.01 Articolo in rivista Sci Rep.pdf41598_2022_11620_MOESM1_ESM.pdf
MCJ/DNAJC15 mitochondrial chaperone as a metabolic “balance needle” in ovarian cancer chemoresistance Stefano Miglietta, Manuela Sollazzo, Lorena Marchio, Iacopo Gherardi, Sara Milioni, Luisa Iommari...ni, Ivana Kurelac, Anna Maria Ghelli, Giuseppe Gasparre, Anna Maria Porcelli 2022-01-01 - - 4.01 Contributo in Atti di convegno -
MicroRNA and Metabolic Profiling of a Primary Ovarian Neuroendocrine Carcinoma Pulmonary-Type Reveals a High Degree of Similarity with Small Cell Lung Cancer Miglietta, Stefano; Girolimetti, Giulia; Marchio, Lorena; Sollazzo, Manuela; Laprovitera, Noemi; ...Coluccelli, Sara; De Biase, Dario; De Leo, Antonio; Santini, Donatella; Kurelac, Ivana; Iommarini, Luisa; Ghelli, Anna; Campana, Davide; Ferracin, Manuela; Perrone, Anna Myriam; Gasparre, Giuseppe; Porcelli, Anna Maria 2022-01-01 NON-CODING RNA - 1.01 Articolo in rivista NcRNA.pdf
NDUFS3 knockout cancer cells and molecular docking reveal specificity and mode of action of anti-cancer respiratory complex I inhibitors Kurelac, Ivana; Cavina, Beatrice; Sollazzo, Manuela; Miglietta, Stefano; Fornasa, Agnese; De Luis...e, Monica; Iorio, Maria; Lama, Eleonora; Traversa, Daniele; Nasiri, Hamid Razi; Ghelli, Anna; Musiani, Francesco; Porcelli, Anna Maria; Iommarini, Luisa; Gasparre, Giuseppe 2022-01-01 OPEN BIOLOGY - 1.01 Articolo in rivista rsob.220198.pdf
New Insights on Rotenone Resistance of Complex I Induced by the m.11778G>A/MT-ND4 Mutation Associated with Leber’s Hereditary Optic Neuropathy Musiani F.; Rigobello L.; Iommarini L.; Carelli V.; Esposti M.D.; Ghelli A.M. 2022-01-01 MOLECULES - 1.01 Articolo in rivista molecules-27-01341.pdfmolecules-27-01341-s001.zip
Respiratory complex I null cancer cells and molecular docking reveal specificity and mode of action inhibitors with anticancer activity Iommarini, Luisa; Kurelac, Ivana; Cavina, Beatrice; Fornasa, Agnese; Traversa, Daniele; Iorio, Ma...ria; Sollazzo, Manuela; De Luise, Monica; Lama, Eleonora; Nasiri, Hamid Razi; Ghelli, Anna; Musiani, Francesco; Gasparre, Giuseppe; Porcelli, Anna Maria 2022-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 4.02 Riassunto (Abstract) -
Duplexing complexome profiling with SILAC to study human respiratory chain assembly defects Palenikova P.; Harbour M.E.; Prodi F.; Minczuk M.; Zeviani M.; Ghelli A.; Fernandez-Vizarra E. 2021-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.01 Articolo in rivista 2021 - Palenikova - BBA-Bioenerg.pdfMicrosoft Word - SILAC-CP_Supplementary_Figs_Final.docx.pdf
Organization of the respiratory supercomplexes in cells with defective complex III: Structural features and metabolic consequences Rugolo M.; Zanna C.; Ghelli A.M. 2021-01-01 LIFE - 1.01 Articolo in rivista 2021 - Rugolo et al - Review CIII and SCs.pdf
Drug repositioning as a therapeutic strategy for neurodegenerations associated with OPA1 mutations Aleo, Serena J; Del Dotto, Valentina; Fogazza, Mario; Maresca, Alessandra; Lodi, Tiziana; Goffrin...i, Paola; Ghelli, Anna; Rugolo, Michela; Carelli, Valerio; Baruffini, Enrico; Zanna, Claudia 2020-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista 2021 - Aleo et al HMG.pdfsupplementary_material_19-10-20_ddaa244.docx
Exogenous peptides are able to penetrate human cell and mitochondrial membranes, stabilize mitochondrial tRNA structures, and rescue severe mitochondrial defects Perli, Elena; Pisano, Annalinda; Pignataro, Maria Gemma; Campese, Antonio Francesco; Pelullo, Mar...ia; Genovese, Ilaria; de Turris, Valeria; Ghelli, Anna Maria; Cerbelli, Bruna; Giordano, Carla; Colotti, Gianni; Morea, Veronica; d'Amati, Giulia 2020-01-01 THE FASEB JOURNAL - 1.01 Articolo in rivista 2020 - Perli - Exogenous peptides and tRNA mitochondrial defects - FASEB J.pdffsb220504-sup-0006-figs6.tiffsb220504-sup-0003-figs3.tiffsb220504-sup-0004-figs4.tiffsb220504-sup-0005-figs5.tiffsb220504-sup-0002-figs2.tif