RUGOLO, MICHELA
Dettaglio
RUGOLO, MICHELA
DIPARTIMENTO DI FARMACIA E BIOTECNOLOGIE
Pubblicazioni
Risultati 1 - 20 di 72 (tempo di esecuzione: 0.002 secondi).
Titolo | Autore(i) | Anno | Periodico | Editore | Tipo | File | |
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1 | A cellular model for cancer progression: Role of mitochondrial mutations and metabolism | G. Romeo; G. Gasparre; A.M. Porcelli; M. Rugolo | 2010 | JOURNAL OF BIOTECHNOLOGY | 4.02 Riassunto (Abstract) | - | |
2 | A clinically complex form of dominant optic atrophy (OPA8) maps on chromosome 16. | Carelli V.; Schimpf S.; Fuhrmann N.; Valentino M.L.; Zanna C.; Iommarini L.; Papke M.; Schaich S....; Tippmann S.; Baumann B.; Barboni P.; Longanesi L.; Rugolo M.; Ghelli A.; Alavi M.V.; Youle R.J.; Bucchi L.; Carroccia R.; Giannoccaro M.P.; Tonon C.; Lodi R.; Cenacchi G.; Montagna P.; Liguori R.; Wissinger B. | 2011 | HUMAN MOLECULAR GENETICS | 1.01 Articolo in rivista | - | |
3 | AIF and endonuclease G are involved in the caspase-indepenent death of cybrids with LHON mutations | A.M.Porcelli; C. Zanna; A. Montanaro; V.Carelli; A.Ghelli; M.Rugolo | 2004 | s.n | 4.02 Riassunto (Abstract) | - | |
4 | Alterations in the supramolecular interactions of respiratory chain complexes and enhanced superoxide production by the cytochrome b Y278C mutation which causes a multisystem disorder | Ghelli A.; Tropeano C.V.; Calvaruso M.A.; Marchesini A.; Iommarini L.; Porcelli A.M.; Zanna C.; G...asparre G.; Kurelac I.; De Nardo V.; Martinuzzi A.; Vissing J.; Selamoglu N.; Daldal F.; Rugolo M. | 2012 | BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS | 4.02 Riassunto (Abstract) | - | |
5 | The antioxidant function of Bcl-2 preserves cytoskeletal stability of cells with defective respiratory complex I. | Porcelli A.M.; Ghelli A.; Iommarini L.; Mariani E.; Hoque M.; Zanna C.; Gasparre G.; Rugolo M. | 2008 | CELLULAR AND MOLECULAR LIFE SCIENCES | 1.01 Articolo in rivista | - | |
6 | Apoptosis induced by staurosporine in ECV304 cells requires cell shrinkage and upregulation of Cl- conductance | A.M. PORCELLI; A. GHELLI; C. ZANNA; P. VALENTE; S. FERRONI; M. RUGOLO | 2004 | CELL DEATH AND DIFFERENTIATION | 1.01 Articolo in rivista | - | |
7 | ATP depletion and caspase independent death of cybrids bearing Leber's Hereditary Optic neuropathy MTDNA mutations incubated in galactose medium. A model for endonuclease G-mediated apoptosis | A. Ghelli; C. Zanna; A.M. Porcelli; V. Carelli; M. Rugolo | 2004 | Dipartimento Biologia Ev. SP. | 4.02 Riassunto (Abstract) | - | |
8 | The background of mitochondrial DNA haplogroup J increases the sensitivity of Leber's hereditary optic neuropathy cells to 2,5-hexanedione toxicity. | Ghelli A.; Porcelli A.M.; Zanna C.; Vidoni S.; Mattioli S.; Barbieri A.; Iommarini L.; Pala M.; A...chilli A.; Torroni A.; Rugolo M.; Carelli V. | 2009 | PLOS ONE | 1.01 Articolo in rivista | ||
9 | 'Behr syndrome' with OPA1 compound heterozygote mutations | Carelli, Valerio; Sabatelli, Mario; Carrozzo, Rosalba; Rizza, Teresa; Schimpf, Simone; Wissinger,... Bernd; Zanna, Claudia; Rugolo, Michela; La Morgia, Chiara; Caporali, Leonardo; Carbonelli, Michele; Barboni, Piero; Tonon, Caterina; Lodi, Raffaele; Bertini, Enrico | 2015 | BRAIN (ONLINE) | 1.01 Articolo in rivista | - | |
10 | Biochimica | Ascenzi P.; Contestabile R.; Di Salvo M.L.; Faraone Mennella M.R.; Fusi P.; Lenaz G.; Pascarella ...S.; Quesada P.M.; Rugolo M.; Sorrentino S.; Tortora P.; Turina P. | 2007 | Idelson-Gnocchi | 3.02 Curatela | - | |
11 | Bioenergetics shapes cellular death pathways in Leber’s hereditary optic neuropathy: a model of mitochondrial neurodegeneration | CARELLI V; RUGOLO M; SGARBI G; GHELLI A; ZANNA C; BARACCA A; LENAZ G; NAPOLI E; MARTINUZZI A; SOL...AINI G. | 2004 | BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS | 1.01 Articolo in rivista | - | |
12 | Caspase-independent death of Leber's hereditary optic neuropathy cybrids is driven by energetic failure and mediated by AIF and Endonuclease G. | ZANNA C.; GHELLI A.; PORCELLI AM.; MARTINUZZI A.; Carelli V.; RUGOLO M. | 2005 | APOPTOSIS | 1.01 Articolo in rivista | - | |
13 | Cell death of fibroblasts derived from patients with Leber’s hereditary optic neuropathy mtDNA mutations | C.Zanna; A.M.Porcelli; A.Ghelli; V.Carelli; A.Martinuzzi; M.Rugolo | 2004 | s.n | 4.02 Riassunto (Abstract) | - | |
14 | Cellular and mitochondrial determination of low molecular mass organic acids by LC-MS/MS | Fiori, Jessica; Amadesi, Elisa; Fanelli, Flaminia; Tropeano, Concetta Valentina; Rugolo, Michela;... Gotti, Roberto | 2018 | JOURNAL OF PHARMACEUTICAL AND BIOMEDICAL ANALYSIS | 1.01 Articolo in rivista | - | |
15 | Clonal expansion of mtDNA deletions: different disease models assessed by digital droplet PCR in single muscle cells. | Trifunov S., Pyle A., Valentino ML., Liguori R., Yu-Wai-Man P., Burté F., Duff J., Kleinle S., Di...ebold I., Rugolo M., Horvath R., Carelli V. | 2018 | SCIENTIFIC REPORTS | 1.01 Articolo in rivista | ||
16 | Complex II phosphorylation is triggered by unbalanced redox homeostasis in cells lacking complex III | Tropeano, Concetta Valentina; Fiori, Jessica; Carelli, Valerio; Caporali, Leonardo; Daldal, Fevzi...; Ghelli, Anna Maria; Rugolo, Michela | 2018 | BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS | 1.01 Articolo in rivista | - | |
17 | Cybrids with mtDNA mutations causing Leber’s hereditary optic neuropathy are sensitized to apoptotic death induced by a mitochondrial oxidative stress | A. M. Ghelli; C. Zanna; V. Carelli; A. Martinuzzi; M. Rugolo | 2006 | s.n | 4.02 Riassunto (Abstract) | - | |
18 | Deciphering OPA1 mutations pathogenicity by combined analysis of human, mouse and yeast cell models | Del Dotto, Valentina; Fogazza, Mario; Musiani, Francesco; Maresca, Alessandra; Aleo, Serena J.; C...aporali, Leonardo; La Morgia, Chiara; Nolli, Cecilia; Lodi, Tiziana; Goffrini, Paola; Chan, David; Carelli, Valerio; Rugolo, Michela; Baruffini, Enrico; Zanna, Claudia* | 2018 | BIOCHIMICA ET BIOPHYSICA ACTA. MOLECULAR BASIS OF DISEASE | 1.01 Articolo in rivista | ||
19 | Defective oxidative phosphorylation in thyroid oncocytic carcinoma is associated with pathogenic mitochondrial DNA mutations affecting complexes I and III | BONORA E.; PORCELLI A.M.; GASPARRE G.; BIONDI A.; GHELLI A.; CARELLI V.; BARACCA A.; TALLINI G.; ...MARTINUZZI A.; LENAZ G.; RUGOLO M.; ROMEO G. | 2006 | CANCER RESEARCH | 1.01 Articolo in rivista | - | |
20 | Determination of mitochondrial fusion in fibroblasts from dominant optic atrophy patients bearing the c.2708delttag OPA1 mutation | C. Zanna; A. Ghelli; A. M.Porcelli; M. Karbowski; R.J. Youle; V. Carelli; M. Rugolo | 2006 | s. n. | 4.02 Riassunto (Abstract) | - |