RUGOLO, MICHELA
RUGOLO, MICHELA
FABIT - DIPARTIMENTO DI FARMACIA E BIOTECNOLOGIE
Coenzyme Q biosynthesis inhibition induces HIF-1α stabilization and metabolic switch toward glycolysis
2021 Liparulo, Irene; Bergamini, Christian; Bortolus, Marco; Calonghi, Natalia; Gasparre, Giuseppe; Kurelac, Ivana; Masin, Luca; Rizzardi, Nicola; Rugolo, Michela; Wang, Wenping; Aleo, Serena J; Kiwan, Alisar; Torri, Cristian; Zanna, Claudia; Fato, Romana
Organization of the respiratory supercomplexes in cells with defective complex III: Structural features and metabolic consequences
2021 Rugolo M.; Zanna C.; Ghelli A.M.
Drug repositioning as a therapeutic strategy for neurodegenerations associated with OPA1 mutations
2020 Aleo, Serena J; Del Dotto, Valentina; Fogazza, Mario; Maresca, Alessandra; Lodi, Tiziana; Goffrini, Paola; Ghelli, Anna; Rugolo, Michela; Carelli, Valerio; Baruffini, Enrico; Zanna, Claudia
Fine-tuning of the respiratory complexes stability and supercomplexes assembly in cells defective of complex III
2020 Tropeano C.V.; Aleo S.J.; Zanna C.; Roberti M.; Scandiffio L.; Loguercio Polosa P.; Fiori J.; Porru E.; Roda A.; Carelli V.; Steimle S.; Daldal F.; Rugolo M.; Ghelli A.
Metabolomics hallmarks OPA1 variants correlating with their in-vitro phenotype and predicting clinical severity
2020 Barca, Juan Manuel Chao; Fogazza, Mario; Rugolo, Michela; Chupin, Stéphanie; Del Dotto, Valentina; Ghelli, Anna Maria; Carelli, Valerio; Simard, Gilles; Procaccio, Vincent; Bonneau, Dominique; Lenaers, Guy; Reynier, Pascal; Zanna, Claudia
Reactive Oxygen Species Produced by Mutated Mitochondrial Respiratory Chains of Entire Cells Monitored Using Modified Microelectrodes
2019 Malferrari, Marco; Ghelli, Anna*; Roggiani, Francesco; Valenti, Giovanni; Paolucci, Francesco; Rugolo, Michela; Rapino, Stefania
Cellular and mitochondrial determination of low molecular mass organic acids by LC-MS/MS
2018 Fiori, Jessica; Amadesi, Elisa; Fanelli, Flaminia; Tropeano, Concetta Valentina; Rugolo, Michela; Gotti, Roberto
Clonal expansion of mtDNA deletions: different disease models assessed by digital droplet PCR in single muscle cells.
2018 Trifunov S., Pyle A., Valentino ML., Liguori R., Yu-Wai-Man P., Burté F., Duff J., Kleinle S., Diebold I., Rugolo M., Horvath R., Carelli V.
Complex II phosphorylation is triggered by unbalanced redox homeostasis in cells lacking complex III
2018 Tropeano, Concetta Valentina; Fiori, Jessica; Carelli, Valerio; Caporali, Leonardo; Daldal, Fevzi; Ghelli, Anna Maria; Rugolo, Michela
Deciphering OPA1 mutations pathogenicity by combined analysis of human, mouse and yeast cell models
2018 Del Dotto, Valentina; Fogazza, Mario; Musiani, Francesco; Maresca, Alessandra; Aleo, Serena J.; Caporali, Leonardo; La Morgia, Chiara; Nolli, Cecilia; Lodi, Tiziana; Goffrini, Paola; Chan, David; Carelli, Valerio; Rugolo, Michela; Baruffini, Enrico; Zanna, Claudia*
Eight human OPA1 isoforms, long and short: What are they for?
2018 Del Dotto, Valentina; Fogazza, Mario; Carelli, Valerio; Rugolo, Michela; Zanna, Claudia
OPA1: how much do we know to approach therapy?
2018 Del Dotto, Valentina; Fogazza, Mario; Lenaers, Guy; Rugolo, Michela; Carelli, Valerio; Zanna, Claudia
OPA1 Isoforms in the Hierarchical Organization of Mitochondrial Functions
2017 Del Dotto, Valentina; Mishra, Prashant; Vidoni, Sara; Fogazza, Mario; Maresca, Alessandra; Caporali, Leonardo; Mccaffery, J Michael; Cappelletti, Martina; Baruffini, Enrico; Lenaers, Guy; Chan, David; Rugolo, Michela; Carelli, Valerio; Zanna, Claudia
'Behr syndrome' with OPA1 compound heterozygote mutations
2015 Carelli, Valerio; Sabatelli, Mario; Carrozzo, Rosalba; Rizza, Teresa; Schimpf, Simone; Wissinger, Bernd; Zanna, Claudia; Rugolo, Michela; La Morgia, Chiara; Caporali, Leonardo; Carbonelli, Michele; Barboni, Piero; Tonon, Caterina; Lodi, Raffaele; Bertini, Enrico
Mitochondria: Biogenesis and mitophagy balance in segregation and clonal expansion of mitochondrial DNA mutations
2015 Valerio, Carelli; Alessandra, Maresca; Leonardo, Caporali; Selena, Trifunov; Claudia, Zanna; Michela, Rugolo
Mitochondrial Respiratory Supercomplexes in Physiology and Diseases
2015 Ghelli, Anna Maria; Valentina C. Tropeano; Rugolo, Michela
Syndromic parkinsonism and dementia associated with OPA1 missense mutations
2015 Carelli, V.; Musumeci, O.; Caporali, L.; Zanna, C.; La Morgia, C.; Del Dotto, V.; Porcelli, A.M.; Rugolo, M.; Valentino, M.L.; Iommarini, L.; Maresca, A.; Barboni, P.; Carbonelli, M.; Trombetta, C.; Valente, E.M.; Patergnani, S.; Giorgi, C.; Pinton, P.; Rizzo, G.; Tonon, C.; Lodi, R.; Avoni, P.; Liguori, R.; Baruzzi, A.; Toscano, A.; Zeviani, M.
A novel in-frame 18-bp microdeletion in MT-CYB causes a multisystem disorder with prominent exercise intolerance.
2014 Carossa V;Ghelli A;Tropeano CV;Valentino ML;Iommarini L;Maresca A;Caporali L;Morgia CL;Liguori R;Barboni P;Carbonelli M;Rizzo G;Tonon C;Lodi R;Martinuzzi A;Nardo VD;Rugolo M;Ferretti L;Gandini F;Pala M;Achilli A;Olivieri A;Torroni A;Carelli V
Different mtDNA mutations modify tumor progression in dependence of the degree of respiratory complex I impairment
2014 L. Iommarini;I. Kurelac;M. Capristo;M. A. Calvaruso;V. Giorgio;C. Bergamini;A. Ghelli;P. Nanni;C. De Giovanni;V. Carelli;R. Fato;P. L. Lollini;M. Rugolo;G. Gasparre;A. M. Porcelli
Gamma rays induce a p53-independent mitochondrial biogenesis that is counter-regulated by HIF1α.
2013 Bartoletti-Stella A;Mariani E;Kurelac I;Maresca A;Caratozzolo MF;Iommarini L;Carelli V;Eusebi LH;Guido A;Cenacchi G;Fuccio L;Rugolo M;Tullo A;Porcelli AM;Gasparre G