CIANI, ELISABETTA
CIANI, ELISABETTA
DIBINEM - DIPARTIMENTO DI SCIENZE BIOMEDICHE E NEUROMOTORIE
Docenti di ruolo di IIa fascia
Adult-Onset Deletion of CDKL5 in Forebrain Glutamatergic Neurons Impairs Synaptic Integrity and Behavior in Mice
2025 Mottolese, Nicola; Iannibelli, Feliciana; Candini, Giulia; Trebbi, Federica; Loi, Manuela; Bove, Angelica Marina; Medici, Giorgio; Xiong, Zhi-Qi; Ciani, Elisabetta; Trazzi, Stefania
AR-A014418-based dual Glycogen Synthase Kinase 3β/Histone Deacetylase inhibitors as potential therapeutics for Alzheimer's disease
2025 Santini, Alan; Tassinari, Elisa; Altomare, Alessandra; Loi, Manuela; Ciani, Elisabetta; Trazzi, Stefania; Piccarducci, Rebecca; Daniele, Simona; Martini, Claudia; Pagliarani, Barbara; Tarozzi, Andrea; Bersani, Matteo; Spyrakis, Francesca; Danková, Daniela; Poeta, Eleonora; Raimondi, Simone; Davani, Lara; Aldini, Giancarlo; Andrisano, Vincenza; De Simone, Angela; Milelli, Andrea
Beneficial Antioxidant Effects of Coenzyme Q10 in In Vitro and In Vivo Models of CDKL5 Deficiency Disorder
2025 Loi, Manuela; Valenti, Francesca; Medici, Giorgio; Mottolese, Nicola; Candini, Giulia; Bove, ANGELICA MARINA; Trebbi, Federica; Pincigher, Luca; Fato, Romana; Bergamini, Christian; Trazzi, Stefania; Ciani, Elisabetta
Design, synthesis and pharmacological evaluation of multitarget GPR40 agonists/HDAC6 inhibitors for Alzheimer's disease
2025 Pinheiro, P. D. S. M.; De Chirico, F.; Loi, M.; Trazzi, S.; Ciani, E.; Rodrigues, D. A.; Alves, M. A.; Lima, L. M.; Milelli, A.; Monti, B.; Manssour Fraga, C. A.; Bolognesi, M. L.
Lactic acid bacteria as microbial cell factories for the in vivo delivery of therapeutic proteins as secretable TAT fusion products
2025 Medici, Giorgio; Candini, Giulia; Mottolese, Nicola; Uguagliati, Beatrice; Trebbi, Federica; Loi, Manuela; Bove, Angelica Marina; Stojanov, Spase; Esposito, Erika; Vitagliano, Rosalba; D'Amico, Federica; Turroni, Silvia; Fiori, Jessica; Berlec, Aleš; Trazzi, Stefania; Ciani, Elisabetta
Safety and efficacy of Igk-TATk-CDKL5 gene therapy in mosaic CDKL5 deficiency
2025 Medici, Giorgio; Tassinari, Marianna; Loi, Manuela; Bove, Angelica Marina; Garofani, Beatrice Casadei; Volpedo, Greta; Mottolese, Nicola; Matteoli, Gabriele; Lo Martire, Viviana; Berteotti, Chiara; Candini, Giulia; Trebbi, Federica; Riva, Antonella; Striano, Pasquale; Zoccoli, Giovanna; Curia, Giulia; Trazzi, Stefania; Ciani, Elisabetta
Autistic-relevant behavioral phenotypes of a mouse model of cyclin-dependent kinase-like 5 deficiency disorder
2024 Mottolese N.; Coiffard O.; Ferraguto C.; Manolis A.; Ciani E.; Pietropaolo S.
Characterisation of sleep apneas and respiratory circuitry in mice lacking CDKL5
2024 Matteoli, G.; Alvente, S.; Bastianini, S.; Berteotti, C.; Ciani, E.; Cinelli, E.; Lo Martire, V.; Medici, G.; Mello, T.; Miglioranza, E.; Silvani, A.; Mutolo, D.; Zoccoli, G.
Effects of a ciliary neurotrophic factor (CNTF) small-molecule peptide mimetic in an in vitro and in vivo model of CDKL5 deficiency disorder
2024 Mottolese, Nicola; Loi, Manuela; Trazzi, Stefania; Tassinari, Marianna; Uguagliati, Beatrice; Candini, Giulia; Iqbal, Khalid; Medici, Giorgio; Ciani, Elisabetta
First in Class Dual Non-ATP-Competitive Glycogen Synthase Kinase 3β/Histone Deacetylase Inhibitors as a Potential Therapeutic to Treat Alzheimer’s Disease
2024 Santini, A.; Tassinari, E.; Poeta, E.; Loi, M.; Ciani, E.; Trazzi, S.; Piccarducci, R.; Daniele, S.; Martini, C.; Pagliarani, B.; Tarozzi, A.; Bersani, M.; Spyrakis, F.; Danková, D.; Olsen, C. A.; Soldati, R.; Tumiatti, V.; Montanari, S.; De Simone, A.; Milelli, A.
Therapeutic efficacy of the BKCa channel opener chlorzoxazone in a mouse model of Fragile X syndrome
2024 Ferraguto C.; Piquemal-Lagoueillat M.; Lemaire V.; Moreau M.M.; Trazzi S.; Uguagliati B.; Ciani E.; Bertrand S.S.; Louette E.; Bontempi B.; Pietropaolo S.
Cardiac Functional and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder
2023 Loi, Manuela; Bastianini, Stefano; Candini, Giulia; Rizzardi, Nicola; Medici, Giorgio; Papa, Valentina; Gennaccaro, Laura; Mottolese, Nicola; Tassinari, Marianna; Uguagliati, Beatrice; Berteotti, Chiara; Martire, Viviana Lo; Zoccoli, Giovanna; Cenacchi, Giovanna; Trazzi, Stefania; Bergamini, Christian; Ciani, Elisabetta
Characterization of Perinatal Stem Cell Spheroids for the Development of Cell Therapy Strategy
2023 Francesca Paris; Pasquale Marrazzo; Valeria Pizzuti; Cosetta Marchionni; Maura Rossi; Martina Michelotti; Biljana Petrovic; Elisabetta Ciani; Giuliana Simonazzi; Andrea Pession; Laura Bonsi; Francesco Alviano
Early-onset brain alterations during postnatal development in a mouse model of CDKL5 deficiency disorder
2023 Tassinari, Marianna; Uguagliati, Beatrice; Trazzi, Stefania; Cerchier, Camilla Bruna; Cavina, Ottavia Vera; Mottolese, Nicola; Loi, Manuela; Candini, Giulia; Medici, Giorgio; Ciani, Elisabetta
Voluntary Running Improves Behavioral and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder
2023 Mottolese, Nicola; Uguagliati, Beatrice; Tassinari, Marianna; Cerchier, Camilla Bruna; Loi, Manuela; Candini, Giulia; Rimondini, Roberto; Medici, Giorgio; Trazzi, Stefania; Ciani, Elisabetta
Artificial protein and its applications
2022 Alessandro Silvani; Giuseppe Plazzi; Giorgio Medici; Stefania Trazzi; Elisabetta Ciani; Gabriele Matteoli; Sara Alvente; Viviana Lo Martire; Stefano Bastianini; Chiara Berteotti; Giovanna Zoccoli
Expression of a Secretable, Cell-Penetrating CDKL5 Protein Enhances the Efficacy of Gene Therapy for CDKL5 Deficiency Disorder
2022 Medici, Giorgio; Tassinari, Marianna; Galvani, Giuseppe; Bastianini, Stefano; Gennaccaro, Laura; Loi, Manuela; Mottolese, Nicola; Alvente, Sara; Berteotti, Chiara; Sagona, Giulia; Lupori, Leonardo; Candini, Giulia; Baggett, Helen Rappe; Zoccoli, Giovanna; Giustetto, Maurizio; Muotri, Alysson; Pizzorusso, Tommaso; Nakai, Hiroyuki; Trazzi, Stefania; Ciani, Elisabetta
Luteolin Treatment Ameliorates Brain Development and Behavioral Performance in a Mouse Model of CDKL5 Deficiency Disorder
2022 Tassinari, Marianna; Mottolese, Nicola; Galvani, Giuseppe; Ferrara, Domenico; Gennaccaro, Laura; Loi, Manuela; Medici, Giorgio; Candini, Giulia; Rimondini, Roberto; Ciani, Elisabetta; Trazzi, Stefania
Treatment with FRAX486 rescues neurobehavioral and metabolic alterations in a female mouse model of CDKL5 deficiency disorder
2022 Fuchs, Claudia; Cosentino, Livia; Urbinati, Chiara; Talamo, Maria Cristina; Medici, Giorgio; Quattrini, Maria Cristina; Mottolese, Nicola; Pietraforte, Donatella; Fuso, Andrea; Ciani, Elisabetta; De Filippis, Bianca
A GABAB receptor antagonist rescues functional and structural impairments in the perirhinal cortex of a mouse model of CDKL5 deficiency disorder
2021 Laura Gennaccaro, Claudia Fuchs, Manuela Loi, Vincenzo Roncacè, Stefania Trazzi, Yassine Ait-Bali, Giuseppe Galvani, Anna Cecilia Berardi, Giorgio Medici, Marianna Tassinari, Elisa Ren, Roberto Rimondini, Maurizio Giustetto, Giorgio Aicardi, Elisabetta Ciani
| Titolo | Autore(i) | Anno | Periodico | Editore | Tipo | File |
|---|---|---|---|---|---|---|
| Adult-Onset Deletion of CDKL5 in Forebrain Glutamatergic Neurons Impairs Synaptic Integrity and Behavior in Mice | Mottolese, Nicola; Iannibelli, Feliciana; Candini, Giulia; Trebbi, Federica; Loi, Manuela; Bove, ...Angelica Marina; Medici, Giorgio; Xiong, Zhi-Qi; Ciani, Elisabetta; Trazzi, Stefania | 2025-01-01 | INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES | - | 1.01 Articolo in rivista | ijms-26-06626-manuscript.pdf; ijms-3733101-supplementary.pdf |
| AR-A014418-based dual Glycogen Synthase Kinase 3β/Histone Deacetylase inhibitors as potential therapeutics for Alzheimer's disease | Santini, Alan; Tassinari, Elisa; Altomare, Alessandra; Loi, Manuela; Ciani, Elisabetta; Trazzi, S...tefania; Piccarducci, Rebecca; Daniele, Simona; Martini, Claudia; Pagliarani, Barbara; Tarozzi, Andrea; Bersani, Matteo; Spyrakis, Francesca; Danková, Daniela; Poeta, Eleonora; Raimondi, Simone; Davani, Lara; Aldini, Giancarlo; Andrisano, Vincenza; De Simone, Angela; Milelli, Andrea | 2025-01-01 | EUROPEAN JOURNAL OF MEDICINAL CHEMISTRY | - | 1.01 Articolo in rivista | AR-A014418-based dual Glycogen Synthase Kinase 3β_Histone Deacetylase inhibitors as potential therapeutics for Alzheimer_s disease.pdf; 1-s2.0-S0223523425006038-mmc1.docx |
| Beneficial Antioxidant Effects of Coenzyme Q10 in In Vitro and In Vivo Models of CDKL5 Deficiency Disorder | Loi, Manuela; Valenti, Francesca; Medici, Giorgio; Mottolese, Nicola; Candini, Giulia; Bove, ANGE...LICA MARINA; Trebbi, Federica; Pincigher, Luca; Fato, Romana; Bergamini, Christian; Trazzi, Stefania; Ciani, Elisabetta | 2025-01-01 | INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES | - | 1.01 Articolo in rivista | ijms-26-02204-v3.pdf; ijms-26-02204-s001.zip |
| Design, synthesis and pharmacological evaluation of multitarget GPR40 agonists/HDAC6 inhibitors for Alzheimer's disease | Pinheiro, P. D. S. M.; De Chirico, F.; Loi, M.; Trazzi, S.; Ciani, E.; Rodrigues, D. A.; Alves, M.... A.; Lima, L. M.; Milelli, A.; Monti, B.; Manssour Fraga, C. A.; Bolognesi, M. L. | 2025-01-01 | EUROPEAN JOURNAL OF MEDICINAL CHEMISTRY | - | 1.01 Articolo in rivista | - |
| Lactic acid bacteria as microbial cell factories for the in vivo delivery of therapeutic proteins as secretable TAT fusion products | Medici, Giorgio; Candini, Giulia; Mottolese, Nicola; Uguagliati, Beatrice; Trebbi, Federica; Loi,... Manuela; Bove, Angelica Marina; Stojanov, Spase; Esposito, Erika; Vitagliano, Rosalba; D'Amico, Federica; Turroni, Silvia; Fiori, Jessica; Berlec, Aleš; Trazzi, Stefania; Ciani, Elisabetta | 2025-01-01 | JOURNAL OF BIOLOGICAL ENGINEERING | - | 1.01 Articolo in rivista | 13036_2025_Article_538.pdf; 13036_2025_538_MOESM1_ESM.pdf |
| Safety and efficacy of Igk-TATk-CDKL5 gene therapy in mosaic CDKL5 deficiency | Medici, Giorgio; Tassinari, Marianna; Loi, Manuela; Bove, Angelica Marina; Garofani, Beatrice Cas...adei; Volpedo, Greta; Mottolese, Nicola; Matteoli, Gabriele; Lo Martire, Viviana; Berteotti, Chiara; Candini, Giulia; Trebbi, Federica; Riva, Antonella; Striano, Pasquale; Zoccoli, Giovanna; Curia, Giulia; Trazzi, Stefania; Ciani, Elisabetta | 2025-01-01 | NEUROTHERAPEUTICS | - | 1.01 Articolo in rivista | - |
| Autistic-relevant behavioral phenotypes of a mouse model of cyclin-dependent kinase-like 5 deficiency disorder | Mottolese N.; Coiffard O.; Ferraguto C.; Manolis A.; Ciani E.; Pietropaolo S. | 2024-01-01 | AUTISM RESEARCH | - | 1.01 Articolo in rivista | - |
| Characterisation of sleep apneas and respiratory circuitry in mice lacking CDKL5 | Matteoli, G.; Alvente, S.; Bastianini, S.; Berteotti, C.; Ciani, E.; Cinelli, E.; Lo Martire, V.;... Medici, G.; Mello, T.; Miglioranza, E.; Silvani, A.; Mutolo, D.; Zoccoli, G. | 2024-01-01 | JOURNAL OF SLEEP RESEARCH | - | 1.01 Articolo in rivista | Matteoli2024.pdf |
| Effects of a ciliary neurotrophic factor (CNTF) small-molecule peptide mimetic in an in vitro and in vivo model of CDKL5 deficiency disorder | Mottolese, Nicola; Loi, Manuela; Trazzi, Stefania; Tassinari, Marianna; Uguagliati, Beatrice; Can...dini, Giulia; Iqbal, Khalid; Medici, Giorgio; Ciani, Elisabetta | 2024-01-01 | JOURNAL OF NEURODEVELOPMENTAL DISORDERS | - | 1.01 Articolo in rivista | Mottolese et al., 2024_JNDD_Manuscript.pdf |
| First in Class Dual Non-ATP-Competitive Glycogen Synthase Kinase 3β/Histone Deacetylase Inhibitors as a Potential Therapeutic to Treat Alzheimer’s Disease | Santini, A.; Tassinari, E.; Poeta, E.; Loi, M.; Ciani, E.; Trazzi, S.; Piccarducci, R.; Daniele, ...S.; Martini, C.; Pagliarani, B.; Tarozzi, A.; Bersani, M.; Spyrakis, F.; Danková, D.; Olsen, C. A.; Soldati, R.; Tumiatti, V.; Montanari, S.; De Simone, A.; Milelli, A. | 2024-01-01 | ACS CHEMICAL NEUROSCIENCE | - | 1.01 Articolo in rivista | acs-cn.pdf |
| Therapeutic efficacy of the BKCa channel opener chlorzoxazone in a mouse model of Fragile X syndrome | Ferraguto C.; Piquemal-Lagoueillat M.; Lemaire V.; Moreau M.M.; Trazzi S.; Uguagliati B.; Ciani E....; Bertrand S.S.; Louette E.; Bontempi B.; Pietropaolo S. | 2024-01-01 | NEUROPSYCHOPHARMACOLOGY | - | 1.01 Articolo in rivista | - |
| Cardiac Functional and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder | Loi, Manuela; Bastianini, Stefano; Candini, Giulia; Rizzardi, Nicola; Medici, Giorgio; Papa, Vale...ntina; Gennaccaro, Laura; Mottolese, Nicola; Tassinari, Marianna; Uguagliati, Beatrice; Berteotti, Chiara; Martire, Viviana Lo; Zoccoli, Giovanna; Cenacchi, Giovanna; Trazzi, Stefania; Bergamini, Christian; Ciani, Elisabetta | 2023-01-01 | INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES | - | 1.01 Articolo in rivista | 2023, Cardiac Functional and Structural Abnormalities, Loi-Bastianini.pdf; ijms-24-05552-s001.zip |
| Characterization of Perinatal Stem Cell Spheroids for the Development of Cell Therapy Strategy | Francesca Paris; Pasquale Marrazzo; Valeria Pizzuti; Cosetta Marchionni; Maura Rossi; Martina Mic...helotti; Biljana Petrovic; Elisabetta Ciani; Giuliana Simonazzi; Andrea Pession; Laura Bonsi; Francesco Alviano | 2023-01-01 | BIOENGINEERING | - | 1.01 Articolo in rivista | Bioengineering 2023, 10(2), 189;.pdf |
| Early-onset brain alterations during postnatal development in a mouse model of CDKL5 deficiency disorder | Tassinari, Marianna; Uguagliati, Beatrice; Trazzi, Stefania; Cerchier, Camilla Bruna; Cavina, Ott...avia Vera; Mottolese, Nicola; Loi, Manuela; Candini, Giulia; Medici, Giorgio; Ciani, Elisabetta | 2023-01-01 | NEUROBIOLOGY OF DISEASE | - | 1.01 Articolo in rivista | 2023, Early-onset brain alterations during postnatal development in a mouse, Tassinari-Uguagliati.pdf; ScienceDirect_files_24Jul2023_10-41-05.864.zip |
| Voluntary Running Improves Behavioral and Structural Abnormalities in a Mouse Model of CDKL5 Deficiency Disorder | Mottolese, Nicola; Uguagliati, Beatrice; Tassinari, Marianna; Cerchier, Camilla Bruna; Loi, Manue...la; Candini, Giulia; Rimondini, Roberto; Medici, Giorgio; Trazzi, Stefania; Ciani, Elisabetta | 2023-01-01 | BIOMOLECULES | - | 1.01 Articolo in rivista | biomolecules-13-01396.pdf |
| Artificial protein and its applications | Alessandro Silvani; Giuseppe Plazzi; Giorgio Medici; Stefania Trazzi; Elisabetta Ciani; Gabriele ...Matteoli; Sara Alvente; Viviana Lo Martire; Stefano Bastianini; Chiara Berteotti; Giovanna Zoccoli | 2022-01-01 | - | - | 6.01 Brevetto | - |
| Expression of a Secretable, Cell-Penetrating CDKL5 Protein Enhances the Efficacy of Gene Therapy for CDKL5 Deficiency Disorder | Medici, Giorgio; Tassinari, Marianna; Galvani, Giuseppe; Bastianini, Stefano; Gennaccaro, Laura; ...Loi, Manuela; Mottolese, Nicola; Alvente, Sara; Berteotti, Chiara; Sagona, Giulia; Lupori, Leonardo; Candini, Giulia; Baggett, Helen Rappe; Zoccoli, Giovanna; Giustetto, Maurizio; Muotri, Alysson; Pizzorusso, Tommaso; Nakai, Hiroyuki; Trazzi, Stefania; Ciani, Elisabetta | 2022-01-01 | NEUROTHERAPEUTICS | - | 1.01 Articolo in rivista | s13311-022-01295-8.pdf; supplemantary materials.zip |
| Luteolin Treatment Ameliorates Brain Development and Behavioral Performance in a Mouse Model of CDKL5 Deficiency Disorder | Tassinari, Marianna; Mottolese, Nicola; Galvani, Giuseppe; Ferrara, Domenico; Gennaccaro, Laura; ...Loi, Manuela; Medici, Giorgio; Candini, Giulia; Rimondini, Roberto; Ciani, Elisabetta; Trazzi, Stefania | 2022-01-01 | INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES | - | 1.01 Articolo in rivista | ijms-23-08719.pdf; ijms-23-08719-s001.zip |
| Treatment with FRAX486 rescues neurobehavioral and metabolic alterations in a female mouse model of CDKL5 deficiency disorder | Fuchs, Claudia; Cosentino, Livia; Urbinati, Chiara; Talamo, Maria Cristina; Medici, Giorgio; Quat...trini, Maria Cristina; Mottolese, Nicola; Pietraforte, Donatella; Fuso, Andrea; Ciani, Elisabetta; De Filippis, Bianca | 2022-01-01 | CNS NEUROSCIENCE & THERAPEUTICS | - | 1.01 Articolo in rivista | CNS-28-1718.pdf; file supplementare.zip |
| A GABAB receptor antagonist rescues functional and structural impairments in the perirhinal cortex of a mouse model of CDKL5 deficiency disorder | Laura Gennaccaro, Claudia Fuchs, Manuela Loi, Vincenzo Roncacè, Stefania Trazzi, Yassine Ait-Bali..., Giuseppe Galvani, Anna Cecilia Berardi, Giorgio Medici, Marianna Tassinari, Elisa Ren, Roberto Rimondini, Maurizio Giustetto, Giorgio Aicardi, Elisabetta Ciani | 2021-01-01 | NEUROBIOLOGY OF DISEASE | - | 1.01 Articolo in rivista | Gennaccaro et al 2021GABA.pdf; Supplementary data.docx |