Primary perivascular epithelioid cell tumors (PECo- mas) are a variety of rare mesenchymal neoplasm about which very little is known. Due to the small number of cases reported in the literature, there is no consensus about a classi fi cation of this disease that might in fl uence clinical practice and disease management. This article describes a primary PEComa of the bladder in which surgical strategy has been adopted. This strategy has shown good results, showing no local or distant relapse after 2 years of follow-up, without the need of adjuvant therapy. This might be the correct strategy in the treatment of urinary PEComas.
Creti, S., Romagnoli, D., Severini, E., Baldoni, C., Bondi, A., Di Campli, A., et al. (2017). Primary Perivascular Epithelioid Cell Tumor (PEComa) of the Bladder: A Case Report With 2-Years of Follow-Up and Review of Current Literature. CLINICAL GENITOURINARY CANCER, 15(1), 79-81 [10.1016/j.clgc.2016.08.010].
Primary Perivascular Epithelioid Cell Tumor (PEComa) of the Bladder: A Case Report With 2-Years of Follow-Up and Review of Current Literature
ROMAGNOLI, DANIELE;GENTILE, GIORGIO;SCHIAVINA, RICCARDO;BRUNOCILLA, EUGENIO;
2017
Abstract
Primary perivascular epithelioid cell tumors (PECo- mas) are a variety of rare mesenchymal neoplasm about which very little is known. Due to the small number of cases reported in the literature, there is no consensus about a classi fi cation of this disease that might in fl uence clinical practice and disease management. This article describes a primary PEComa of the bladder in which surgical strategy has been adopted. This strategy has shown good results, showing no local or distant relapse after 2 years of follow-up, without the need of adjuvant therapy. This might be the correct strategy in the treatment of urinary PEComas.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
