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Titolo Autore(i) Anno Periodico Editore Tipo File
A Mutation Threshold Distinguishes the Antitumorigenic Effects of the Mitochondrial Gene MTND1, an Oncojanus Function Gasparre G; Kurelac I; Capristo M; Iommarini L; Ghelli A; Ceccarelli C; Nicoletti G; Nanni P; De ...Giovanni C; Scotlandi K; Betts CM; Carelli V; Lollini PL; Romeo G; Rugolo M; Porcelli AM 2011-01-01 CANCER RESEARCH - 1.01 Articolo in rivista -
Mitochondrial complex I and cell death: a semi-automatic shogun model Gonzalez-Halphen D; Ghelli A; Iommarini L; Carelli V; Degli Esposti M 2011-01-01 CELL DEATH & DISEASE - 1.01 Articolo in rivista cddis2011107.pdf
Alterations in the supramolecular interactions of respiratory chain complexes and enhanced superoxide production by the cytochrome b Y278C mutation which causes a multisystem disorder Ghelli A.; Tropeano C.V.; Calvaruso M.A.; Marchesini A.; Iommarini L.; Porcelli A.M.; Zanna C.; G...asparre G.; Kurelac I.; De Nardo V.; Martinuzzi A.; Vissing J.; Selamoglu N.; Daldal F.; Rugolo M. 2012-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 4.02 Riassunto (Abstract) -
The effects of idebenone on mitochondrial bioenergetics Giorgio V; Petronilli V; Ghelli A; Carelli V; Rugolo M; Lenaz G; Bernardi P 2012-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.01 Articolo in rivista -
Cybrid studies establish the causal link between the mtDNA m.3890G>A/MT-ND1 mutation and optic atrophy with bilateral brainstem lesions. Caporali L;Ghelli AM;Iommarini L;Maresca A;Valentino ML;La Morgia C;Liguori R;Zanna C;Barboni P;D...e Nardo V;Martinuzzi A;Rizzo G;Tonon C;Lodi R;Calvaruso MA;Cappelletti M;Porcelli AM;Achilli A;Pala M;Torroni A;Carelli V 2013-01-01 BIOCHIMICA ET BIOPHYSICA ACTA. MOLECULAR BASIS OF DISEASE - 1.01 Articolo in rivista -
Respiratory complex I is essential to induce a Warburg profile in mitochondria-defective tumor cells Calabrese C.; Iommarini L.; Kurelac I.; Calvaruso M.A.; Capristo M.; Lollini P.L.; Nanni P.; Berg...amini C.; Nicoletti G.; De Giovanni C.; Ghelli A.; Giorgio V.; Caratozzolo M.F.; Marzano F.; Manzari C.; Betts C.M.; Carelli V.; Ceccarelli C.; Attimonelli M.; Romeo G.; Fato R.; Rugolo M.; Tullo A.; Gasparre G.; Porcelli A.M. 2013-01-01 CANCER & METABOLISM - 1.01 Articolo in rivista Respiratory complex I is essential to induce a Warburg profile in mitochondria-defective tumor cells.pdfElectronic supplementary material.zip
The cytochrome B p.278Y>C mutation causative of a multisystem disorder enhances superoxide production and alters supramolecular interactions of respiratory chain complexes Ghelli A.; Tropeano C.V.; Calvaruso M.A.; Marchesini A.; Iommarini L.; Porcelli A.M.; Zanna C.; D...e Nardo V.; Martinuzzi A.; Wibrand F.; Vissing J.; Kurelac I.; Gasparre G.; Selamoglu N.; Daldal F.; Rugolo M. 2013-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista -
Molecular mechanisms of superoxide production by complex III: A bacterial versus human mitochondrial comparative case study. Lanciano P; Khalfaoui-Hassani B; Selamoglu N; Ghelli A; Rugolo M; Daldal F 2013-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.01 Articolo in rivista -
Different mtDNA mutations modify tumor progression in dependence of the degree of respiratory complex I impairment L. Iommarini;I. Kurelac;M. Capristo;M. A. Calvaruso;V. Giorgio;C. Bergamini;A. Ghelli;P. Nanni;C.... De Giovanni;V. Carelli;R. Fato;P. L. Lollini;M. Rugolo;G. Gasparre;A. M. Porcelli 2014-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista -
A novel in-frame 18-bp microdeletion in MT-CYB causes a multisystem disorder with prominent exercise intolerance. Carossa V;Ghelli A;Tropeano CV;Valentino ML;Iommarini L;Maresca A;Caporali L;Morgia CL;Liguori R;...Barboni P;Carbonelli M;Rizzo G;Tonon C;Lodi R;Martinuzzi A;Nardo VD;Rugolo M;Ferretti L;Gandini F;Pala M;Achilli A;Olivieri A;Torroni A;Carelli V 2014-01-01 HUMAN MUTATION - 1.01 Articolo in rivista -
Mitochondrial Respiratory Supercomplexes in Physiology and Diseases Ghelli, Anna Maria; Valentina C. Tropeano; Rugolo, Michela 2015-01-01 - Ricardo O. Louro; Irene Diaz-Moreno 2.01 Capitolo / saggio in libro -
Targeting estrogen receptor β as preventive therapeutic strategy for Leber's hereditary optic neuropathy Pisano, Annalinda; Preziuso, Carmela; Iommarini, Luisa; Perli, Elena; Grazioli, Paola; Campese, A...ntonio F; Maresca, Alessandra; Montopoli, Monica; Masuelli, Laura; Sadun, Alfredo A; D'Amati, Giulia; Carelli, Valerio; Ghelli, Anna; Giordano, Carla 2015-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista -
Cigarette toxicity triggers Leber's hereditary optic neuropathy by affecting mtDNA copy number, oxidative phosphorylation and ROS detoxification pathways Giordano, L; Deceglie, S; D'Adamo, P; Valentino, M L; La Morgia, C; Fracasso, F; Roberti, M; Capp...ellari, M; Petrosillo, G; Ciaravolo, S; Parente, D; Giordano, C; Maresca, A; Iommarini, L; Del Dotto, V; Ghelli, A M; Salomao, S R; Berezovsky, A; Belfort, R; Sadun, A A; Carelli, V; Loguercio Polosa, P; Cantatore, P 2015-01-01 CELL DEATH & DISEASE - 1.01 Articolo in rivista Cigarette toxicity triggers Leber's hereditary optic neuropathy.pdfSupplementary information.zip
Melanopsin-expressing retinal ganglion cells are resistant to cell injury, but not always Georg, Birgitte; Ghelli, ANNA MARIA; Giordano, Carla; Ross Cisneros, Fred N.; Sadun, Alfredo A.; ...Carelli, Valerio; Hannibal, Jens; LA MORGIA, Chiara 2017-01-01 MITOCHONDRION - 1.01 Articolo in rivista -
Mitochondrial metabolism and energy sensing in tumor progression Iommarini, Luisa; Ghelli, Anna; Gasparre, Giuseppe; Porcelli, Anna Maria 2017-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.01 Articolo in rivista 1-s2.0-S0005272817300282-main.pdf1-s2.0-S0005272817300282-mmc2.docx
Mild phenotypes and proper supercomplex assembly in human cells carrying the homoplasmic m.15557G > A mutation in cytochrome b gene Iommarini, Luisa; Ghelli, Anna; Leone, Giulia; Tropeano, Concetta Valentina; Kurelac, Ivana; Amat...o, Laura Benedetta; Gasparre, Giuseppe; Porcelli, Anna Maria 2018-01-01 HUMAN MUTATION - 1.01 Articolo in rivista -
Unravelling the Effects of the Mutation m.3571insC/MT-ND1 on Respiratory Complexes Structural Organization Iommarini, Luisa; Ghelli, Anna; Tropeano, Concetta; Kurelac, Ivana; Leone, Giulia; Vidoni, Sara; ...Lombes, Anne; Zeviani, Massimo; Gasparre, Giuseppe; Porcelli, Anna 2018-01-01 INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES - 1.01 Articolo in rivista ijms-19-00764.pdf
Complex II phosphorylation is triggered by unbalanced redox homeostasis in cells lacking complex III Tropeano, Concetta Valentina; Fiori, Jessica; Carelli, Valerio; Caporali, Leonardo; Daldal, Fevzi...; Ghelli, Anna Maria; Rugolo, Michela 2018-01-01 BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS - 1.01 Articolo in rivista -
Haplogroup J mitogenomes are the most sensitive to the pesticide rotenone: Relevance for human diseases Strobbe, Daniela; Caporali, Leonardo; Iommarini, Luisa; Maresca, Alessandra; Montopoli, Monica; M...artinuzzi, Andrea; Achilli, Alessandro; Olivieri, Anna; Torroni, Antonio; Carelli, Valerio; Ghelli, Anna 2018-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista 2018 - Strobbe NeurobDis.pdf
Manipulation of Mitochondria Dynamics Reveals Separate Roles for Form and Function in Mitochondria Distribution Trevisan, Tatiana; Pendin, Diana; Montagna, Aldo; Bova, Sergio; Ghelli, Anna Maria; Daga, Andrea* 2018-01-01 CELL REPORTS - 1.01 Articolo in rivista 2018 - Trevisan Cell Reports.pdf
Mostrati risultati da 41 a 60 di 75
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