Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart.

Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach / Iezzi, Federica; Quarti, Andrea; Surace, Chiara; Pozzi, Marco. - In: CASE REPORTS IN CARDIOLOGY. - ISSN 2090-6404. - ELETTRONICO. - 2016:(2016), pp. 2321017.1-2321017.4. [10.1155/2016/2321017]

Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach

Quarti, Andrea
Secondo
Conceptualization
;
2016

Abstract

Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a 7-year-old female with right adrenal cortical carcinoma, involving the right-side heart.
2016
Paediatric Nonfunctioning Adrenocortical Carcinoma with Extension up to Right-Side Heart: Cardiac Surgery Approach / Iezzi, Federica; Quarti, Andrea; Surace, Chiara; Pozzi, Marco. - In: CASE REPORTS IN CARDIOLOGY. - ISSN 2090-6404. - ELETTRONICO. - 2016:(2016), pp. 2321017.1-2321017.4. [10.1155/2016/2321017]
Iezzi, Federica; Quarti, Andrea; Surace, Chiara; Pozzi, Marco
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11585/850418
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