Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.
Raso, I., Quarti, A., Chessa, M., Basile, D.P., Saracino, A., D'Aiello, A.F., et al. (2020). A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle. WORLD JOURNAL FOR PEDIATRIC & CONGENITAL HEART SURGERY, 11(3), 358-360-360 [10.1177/2150135119894292].
A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle
Quarti, AndreaSecondo
Conceptualization
;
2020
Abstract
Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
