Extra-axial chordoma is a chordoma that occurs in non-axial locations. It is a very rare tumor, with 20 cases reported to date; 14 in bone and six in soft tissue. Of the 14 skeletal extra-axial chordomas, ten were intramedullary and four were intracortical. We report the first case of parosteal extra-axial chordoma arising in the second metacarpal bone, expressing brachyury on immunohistochemical analysis, and describe the pathologic and radiologic findings. We suggest that extra-axial chordoma can occur in parosteal bone lesions or the hand, without features of bone distribution or bone-specific sites.
Parosteal extra-axial chordoma of the second metacarpal bone: a case report with literature review / Tsukamoto, Shinji; Vanel, Daniel*; Righi, Alberto; Donati, Davide Maria; Errani, Costantino. - In: SKELETAL RADIOLOGY. - ISSN 0364-2348. - ELETTRONICO. - 47:4(2018), pp. 579-585. [10.1007/s00256-017-2818-z]
Parosteal extra-axial chordoma of the second metacarpal bone: a case report with literature review
Donati, Davide Maria;
2018
Abstract
Extra-axial chordoma is a chordoma that occurs in non-axial locations. It is a very rare tumor, with 20 cases reported to date; 14 in bone and six in soft tissue. Of the 14 skeletal extra-axial chordomas, ten were intramedullary and four were intracortical. We report the first case of parosteal extra-axial chordoma arising in the second metacarpal bone, expressing brachyury on immunohistochemical analysis, and describe the pathologic and radiologic findings. We suggest that extra-axial chordoma can occur in parosteal bone lesions or the hand, without features of bone distribution or bone-specific sites.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
