We report two cases of bilateral cementless total hip arthroplasty in two young women affected by Morquio-Brailsford syndrome. Morquio-Brailsford disease belongs to the mucopolysaccharidoses; it shows growth retardation with disproportional dwarfism. Usually patients are affected by a severe joint degeneration from their 2nd or 3rd decade. Young age, severe dysplasia, and joint size are the main technical problems for a total hip replacement. Accurate radiographic and CT planning allows the use of standard prostheses instead of custom-made ones.
Tassinari E, Boriani L, Traina F, Dallari D, Toni A, Giunti A. (2008). Bilateral total hip arthroplasty in Morquio-Brailsford's Syndrome: a report of two cases. LA CHIRURGIA DEGLI ORGANI DI MOVIMENTO, 92, 123-126 [10.1007/s12306-008-0046-3].
Bilateral total hip arthroplasty in Morquio-Brailsford's Syndrome: a report of two cases
Traina F;TONI, ALDO;GIUNTI, ARMANDO
2008
Abstract
We report two cases of bilateral cementless total hip arthroplasty in two young women affected by Morquio-Brailsford syndrome. Morquio-Brailsford disease belongs to the mucopolysaccharidoses; it shows growth retardation with disproportional dwarfism. Usually patients are affected by a severe joint degeneration from their 2nd or 3rd decade. Young age, severe dysplasia, and joint size are the main technical problems for a total hip replacement. Accurate radiographic and CT planning allows the use of standard prostheses instead of custom-made ones.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.