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Titolo Autore(i) Anno Periodico Editore Tipo File
APP-dependent up-regulation of Ptch1 underlies proliferation impairment of neural precursors in Down syndrome. Trazzi S.; Mitrugno V.M.; Valli E.; Fuchs C.; Rizzi S.; Guidi S.; Perini G.; Bartesaghi R.; Ciani E. 2011-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista -
Early-occurring proliferation defects in peripheral tissues of the Ts65Dn mouse model of Down syndrome are associated with patched1 over expression Fuchs C; Ciani E; Guidi S; Trazzi S; Bartesaghi R 2012-01-01 LABORATORY INVESTIGATION - 1.01 Articolo in rivista -
CDKL5, a novel MYCN-repressed gene, blocks cell cycle and promotes differentiation of neuronal cells VALLI E; TRAZZI S; FUCHS C; ERRIQUEZ D; BARTESAGHI R; PERINI G; CIANI E 2012-01-01 BIOCHIMICA ET BIOPHYSICA ACTA. GENE REGULATORY MECHANISMS - 1.01 Articolo in rivista -
The amyloid precursor protein (APP) triplicated gene impairs neuronal precursor differentiation and neurite development through two different domains in the Ts65Dn mouse model for down syndrome. Trazzi S; Fuchs C; Valli E; Perini G; Bartesaghi R; Ciani E. 2013-01-01 THE JOURNAL OF BIOLOGICAL CHEMISTRY - 1.01 Articolo in rivista -
APP-dependent alteration of GSK3β activity impairs neurogenesis in the Ts65Dn mouse model of Down syndrome. Trazzi S;Fuchs C;De Franceschi M;Mitrugno VM;Bartesaghi R;Ciani E 2014-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista -
Mapping pathological phenotypes in a mouse model of CDKL5 disorder. Amendola E;Zhan Y;Mattucci C;Castroflorio E;Calcagno E;Fuchs C;Lonetti G;Silingardi D;Vyssotski A...L;Farley D;Ciani E;Pizzorusso T;Giustetto M;Gross CT 2014-01-01 PLOS ONE - 1.01 Articolo in rivista 10.1371_journal.pone.0091613.PDF
Loss of CDKL5 impairs survival and dendritic growth of newborn neurons by altering AKT/GSK-3β signaling. Fuchs C;Trazzi S;Torricella R;Viggiano R;De Franceschi M;Amendola E;Gross C;Calzà L;Bartesaghi R;...Ciani E 2014-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista -
Inhibition of GSK3β rescues hippocampal development and learning in a mouse model of CDKL5 disorder Fuchs, C.; Rimondini, R.; Viggiano, R.; Trazzi, S.; De Franceschi, M.; Bartesaghi, R.; Ciani, E. 2015-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista -
HDAC4: a key factor underlying brain developmental alterations in CDKL5 disorder Trazzi, Stefania; Fuchs, Claudia; Viggiano, Rocchina; De Franceschi, Marianna; Valli, Emanuele; J...edynak, Paulina; Hansen, Finn K; Perini, Giovanni; Rimondini, Roberto; Kurz, Thomas; Bartesaghi, Renata; Ciani, Elisabetta 2016-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista -
Treatment with the GSK3-beta inhibitor Tideglusib improves hippocampal development and memory performance in juvenile, but not adult, Cdkl5 knockout mice Fuchs, Claudia; Fustini, Norma; Trazzi, Stefania; Gennaccaro, Laura; Rimondini, Roberto; Ciani, E...lisabetta* 2018-01-01 EUROPEAN JOURNAL OF NEUROSCIENCE - 1.01 Articolo in rivista -
CDKL5 protein substitution therapy rescues neurological phenotypes of a mouse model of CDKL5 disorder Trazzi, Stefania; De Franceschi, Marianna; Fuchs, Claudia; Bastianini, Stefano; Viggiano, Rocchin...a; Lupori, Leonardo; Mazziotti, Raffaele; Medici, Giorgio; Martire, Viviana Lo; Ren, Elisa; Rimondini, Roberto; Zoccoli, Giovanna; Bartesaghi, Renata; Pizzorusso, Tommaso; Ciani, Elisabetta* 2018-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista trazzi2018 .pdf
Heterozygous CDKL5 Knockout Female Mice Are a Valuable Animal Model for CDKL5 Disorder Fuchs, Claudia; Gennaccaro, Laura; Trazzi, Stefania; Bastianini, Stefano; Bettini, Simone; Martir...e, Viviana Lo; Ren, Elisa; Medici, Giorgio; Zoccoli, Giovanna; Rimondini, Roberto; Ciani, Elisabetta* 2018-01-01 NEURAL PLASTICITY - 1.01 Articolo in rivista 9726950(1).pdfSupplementary Materials.zip
Heterozygous CDKL5 Knockout Female Mice Are a Valuable Animal Model for CDKL5 Disorder Fuchs, Claudia; Gennaccaro, Laura; Trazzi, Stefania; Bastianini, Stefano; Bettini, Simone; Lo Mar...tire, Viviana; Ren, Elisa; Medici, Giorgio; Zoccoli, Giovanna; Rimondini, Roberto; Ciani, Elisabetta 2018-01-01 NEURAL PLASTICITY - 1.01 Articolo in rivista -
Site-specific abnormalities in the visual system of a mouse model of CDKL5 deficiency disorder Lupori L.; Sagona G.; Fuchs C.; Mazziotti R.; Stefanov A.; Putignano E.; Napoli D.; Strettoi E.; ...Ciani E.; Pizzorusso T. 2019-01-01 HUMAN MOLECULAR GENETICS - 1.01 Articolo in rivista ddz102.pdfsupplementary_material_ddz102.pdf
Functional and structural impairments in the perirhinal cortex of a mouse model of CDKL5 deficiency disorder are rescued by a TrkB agonist Ren E.; Roncace V.; Trazzi S.; Fuchs C.; Medici G.; Gennaccaro L.; Loi M.; Galvani G.; Ye K.; Rim...ondini R.; Aicardi G.; Ciani E. 2019-01-01 FRONTIERS IN CELLULAR NEUROSCIENCE - 1.01 Articolo in rivista fncel-13-00169.pdf
CDKL5 deficiency predisposes neurons to cell death through the deregulation of SMAD3 signaling (vol 29, pg 658, 2019) Fuchs C.; Medici G.; Trazzi S.; Gennaccaro L.; Galvani G.; Berteotti C.; Ren E.; Loi M.; Ciani E. 2019-01-01 BRAIN PATHOLOGY - 1.01 Articolo in rivista -
Increased DNA Damage and Apoptosis in CDKL5-Deficient Neurons Loi M.; Trazzi S.; Fuchs C.; Galvani G.; Medici G.; Gennaccaro L.; Tassinari M.; Ciani E. 2020-01-01 MOLECULAR NEUROBIOLOGY - 1.01 Articolo in rivista -
Pharmacotherapy with sertraline rescues brain development and behavior in a mouse model of CDKL5 deficiency disorder Fuchs C.; Gennaccaro L.; Ren E.; Galvani G.; Trazzi S.; Medici G.; Loi M.; Conway E.; Devinsky O....; Rimondini R.; Ciani E. 2020-01-01 NEUROPHARMACOLOGY - 1.01 Articolo in rivista -
Functional impairments in the perirhinal cortex of a mouse model of CDKL5 deficiency disorder are ameliorated by a GABAB receptor antagonist Anna Cecilia Berardi, Claudia Fuchs, Laura Gennaccaro, Vincenzo Roncacè, Yassine Aitbali,
Elisa ...
Ren, Stefania Trazzi, Maurizio Giustetto, Giorgio Aicardi, Elisabetta Ciani
2020-01-01 - - 4.03 Poster -
The green tea polyphenol epigallocatechin-3-gallate (EGCG) restores CDKL5-dependent synaptic defects in vitro and in vivo Trovo L.; Fuchs C.; De Rosa R.; Barbiero I.; Tramarin M.; Ciani E.; Rusconi L.; Kilstrup-Nielsen C. 2020-01-01 NEUROBIOLOGY OF DISEASE - 1.01 Articolo in rivista 1-s2.0-S0969996120300668-main.pdf
Mostrati risultati da 1 a 20 di 25
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