Sfoglia per Autore
Rhodamine 123 as a probe of mitochondrial membrane potential: Evaluation of proton flux through F0 during ATP synthesis
2004 Baracca A.; Sgarbi G.; Solaini G.; Lenaz G.
Severe defect of complex I-dependent ATP synthesis shapes the mitochondria-driven path of apoptotic cell death in Leber’s Hereditary Optic Neuropathy.
2004 Carelli V.; Ghelli A.; Baracca A.; Zanna C.; Sgarbi G.; Solaini G.; Lenaz G.; Rugolo M.; Martinuzzi A.
Bioenergetic changes associated with the T8993G mutation of the mtDNA ATP6 gene.
2004 Baracca A.; Sgarbi G.; Lenaz G.; Carelli V.; Solaini G.
Bioenergetics of mitochondrial diseases associated with mtDNA mutations.
2004 Lenaz G.; Baracca A.; Carelli V.; D'Aurelio M.; Sgarbi G.; Solaini G.
Bioenergetics shapes cellular death pathways in Leber’s hereditary optic neuropathy: a model of mitochondrial neurodegeneration
2004 CARELLI V; RUGOLO M; SGARBI G; GHELLI A; ZANNA C; BARACCA A; LENAZ G; NAPOLI E; MARTINUZZI A; SOLAINI G.
Severe impairment of Complex I-driven adenosine triphosphate synthesis in leber hereditarfy optic neuropathy cybrids
2005 Baracca A.; Solaini G.; Sgarbi G.; Lenaz G.; Baruzzi A.; Schapira A.H.; Martinuzzi A.; Carelli V.
mtDNA T>G mutation at the nt8993 of the ATP6 gene impairs the coupling mechanism of the F1F0-ATPase.
2005 Sgarbi G.; Baracca A.; Lenaz G.; Carelli V.; Solaini G.
Pathogenic role and biochemical dysfunctions associated with mtDNA ATP6 gene mutations.
2005 Solaini G.; Baracca A.; Sgarbi G.; Lenaz G.; Carelli V.
What can we learn from the study of the point mutations in the human mitochondrial ATP6 gene ?
2005 Solaini G.; Baracca A.; Sgarbi G.; Carelli V.; Lenaz G.
Inefficient coupling between proton transport and ATP synthesis may be the pathogenic mechanism for NARP and Leigh syndrome resulting from the T8993G mutation in mtDNA
2006 Gianluca Sgarbi; Alessandra Baracca; Giorgio Lenaz; Lucia M. Valentino; Valerio Carelli; Giancarlo Solaini
Comparative bioenergetic studies of cells carrying the 8993T>G or 8993T>C mitochondrial DNA mutations.
2006 Sgarbi G.; Baracca A.; Mattiazzi M.; Carelli V.; Lenaz G.; Solaini G.
Severe ultrastructural mitochondrial changes in lymphoblasts homozygous for Huntington disease mutation
2006 F. Squitieri; M. Cannella; G. Sgarbi; V. Maglione; A. Falleni; P. Lenzi; A. Baracca; G. Cislaghi; C. Saft; G. Ragona; M.A. Russo; L.M. Thompson; G. Solaini; F. Fornai
Biochemical phenotypes associated with the mitochondrial ATP6 gene mutations at nt8993
2007 Baracca A; Sgarbi G; Mattiazzi M; Casalena G; Pagnotta E; Valentino ML; Moggio M; Lenaz G; Carelli V; Solaini G.
Evaluating mitochondrial membrane potential in cells.
2007 Solaini G.; Sgarbi G.; Lenaz G.; Baracca A.
Pathogenic mutations in the mtDNA ATP6 gene and impairment of the ATP synthase energy transduction
2008 Solaini G; Sgarbi G; Casalena G; Lenaz G; Baracca A
The study of the pathogenic mechanism of mitochondrial diseases provides information on basic bioenergetics
2008 Solaini G; Harris DA; Lenaz G; Sgarbi G; Baracca A
Is super-complex organization of the respiratory chain required for optimal electron transfer activity?
2008 M.L. Genova; A. Baracca; A. Biondi; G. Casalena; M. Faccioli; A.I. Falasca; G. Formiggini; G. Sgarbi; G. Solaini; G. Lenaz.
Is supercomplex organization of the respiratory chain required for optimal electron transfer activity?
2008 Genova ML; Baracca A; Biondi A; Casalena G; Faccioli M; Falasca AI; Formiggini G; Sgarbi G; Solaini G; Lenaz G.
A novel deletion in the GTPase domain of OPA1 causes defects in mitochondrial morphology and distribution, but not in function
2008 Spinazzi M; Cazzola S; Bortolozzi M; Baracca A; Loro E; Casarin A; Solaini G; Sgarbi G; Casalena G; Cenacchi G; Malena A; Frezza C; Carrara F; Angelini C; Scorrano L; Salviati L; Vergani L.
Human NARP Mitochondrial Mutation Metabolism Corrected with Alpha-ketoglutarate/aspartarte: A Potential New Therapy
2009 Sgarbi G; Casalena GA; Baracca A; Lenaz G; DiMauro S; Solaini G
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